Diagnostic Radiology/Musculoskeletal Imaging/Tumors Basic/Maffucci syndrome
Maffucci's syndrome is defined as multiple enchondromatosis with soft tissue and visceral hemangiomas. Patients with Maffucci's syndrome are believed to be at far greater risk for malignant transformation than those with Ollier's disease.
Fig. 1 Maffucci's syndrome. Soft tissue masses with phleboliths are consistent with hemangiomas. Note remodeling of underlying bone.
[Enchondromas and Related Disorders] by Jeffrey P. Kanne, M.D., University of Washington Department of Radiology